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| 1. | Title: Mechanisms and consequences of impaired lipid trafficking in Niemann-Pick type C1-deficient mammalian cells
Author(s): Karten B, Peake KB, Vance JE Source: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS Volume: 1791 Issue: 7 Special Issue: Sp. Iss. SI Pages: 659-670 Published: JUL 2009 |
| 2. | Title: Cholesterol homeostasis in neurons and glial cells
Author(s): Vance JE, Hayashi H, Karten B Source: SEMINARS IN CELL & DEVELOPMENTAL BIOLOGY Volume: 16 Issue: 2 Pages: 193-212 Published: APR 2005 |
| 3. | Title: Niemann-Pick disease type C
Author(s): Vanier MT, Millat G Source: CLINICAL GENETICS Volume: 64 Issue: 4 Pages: 269-281 Published: OCT 2003 |
| 4. | Title: Allopregnanolone treatment delays cholesterol accumulation and reduces autophagic/lysosomal dysfunction and inflammation in Npc1-/- mouse brain
Author(s): Liao GH, Cheung S, Galeano J, et al. Source: BRAIN RESEARCH Volume: 1270 Pages: 140-151 Published: MAY 13 2009 |
| 5. | Title: Neuronal loss of Drosophila NPC1a causes cholesterol aggregation and age-progressive neurodegeneration
Author(s): Phillips SE, Woodruff EA, Liang P, et al. Source: JOURNAL OF NEUROSCIENCE Volume: 28 Issue: 26 Pages: 6569-6582 Published: JUN 25 2008 |
| 6. | Title: Recommendations on the diagnosis and management of Niemann-Pick disease type C
Author(s): Wraith JE, Baumgartner MR, Bembi B, et al. Source: MOLECULAR GENETICS AND METABOLISM Volume: 98 Issue: 1-2 Pages: 152-165 Published: SEP-OCT 2009 |
| 7. | Title: MRI detects therapeutic effects in weanling Niemann-Pick type C mice
Author(s): Lope-Piedrafita S, Totenhagen JW, Hicks CM, et al. Source: JOURNAL OF NEUROSCIENCE RESEARCH Volume: 86 Issue: 12 Pages: 2802-2807 Published: SEP 2008 |
| 8. | Title: Cell-autonomous death of cerebellar Purkinje neurons with autophagy in Niemann-Pick type C disease
Author(s): Ko DC, Milenkovic L, Beier SM, et al. Source: PLOS GENETICS Volume: 1 Issue: 1 Pages: 81-95 Published: JUL 2005 |
| 9. | Title: Increased Activity and Altered Subcellular Distribution of Lysosomal Enzymes Determine Neuronal Vulnerability in Niemann-Pick Type C1-Deficient Mice
Author(s): Amritraj A, Peake K, Kodam A, et al. Source: AMERICAN JOURNAL OF PATHOLOGY Volume: 175 Issue: 6 Pages: 2540-2556 Published: DEC 2009 |
| 10. | Title: Astrocyte-only Npc1 reduces neuronal cholesterol and triples life span of Npc1(-/-) mice
Author(s): Zhang M, Strnatka D, Donohue C, et al. Source: JOURNAL OF NEUROSCIENCE RESEARCH Volume: 86 Issue: 13 Pages: 2848-2856 Published: OCT 2008 |
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