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Title: DEVELOPMENT OF MYELIN IN INGERITED DISORDERS OF AMINO ACID METABOLISM - A BIOCHEMICAL INVESTIGATION
Author(s): PRENSKY, AL
Source: ARCHIVES OF NEUROLOGY Volume: 19 Issue: 6 Pages: 552-& Published: 1968
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1. Title: Water apparent diffusion coefficient and T2 changes in the acute stage of maple syrup urine disease: Evidence of intramyelinic and vasogenic-interstitial edema
Author(s): Righini A, Ramenghi LA, Parini R, et al.
Source: JOURNAL OF NEUROIMAGING   Volume: 13   Issue: 2   Pages: 162-165   Published: APR 2003
2. Title: Maple syrup urine disease - Diffusion-weighted and diffusion-tensor magnetic resonance imaging findings
Author(s): Parmar H, Sitoh YY, Ho L
Source: JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY   Volume: 28   Issue: 1   Pages: 93-97   Published: JAN-FEB 2004
3. Title: MYELINATION IN THE DEVELOPING HUMAN BRAIN - BIOCHEMICAL CORRELATES
Author(s): KINNEY HC, KARTHIGASAN J, BORENSHTEYN NI, et al.
Source: NEUROCHEMICAL RESEARCH   Volume: 19   Issue: 8   Pages: 983-996   Published: AUG 1994
4. Title: IS DEMYELINATION A FEATURE OF MAPLE-SYRUP-URINE-DISEASE
Author(s): MULLER K, KAHN T, WENDEL U
Source: PEDIATRIC NEUROLOGY   Volume: 9   Issue: 5   Pages: 375-382   Published: SEP-OCT 1993
5. Title: ABNORMAL DENDRITIC DEVELOPMENT IN MAPLE SYRUP URINE DISEASE
Author(s): KAMEI A, TAKASHIMA S, CHAN F, et al.
Source: PEDIATRIC NEUROLOGY   Volume: 8   Issue: 2   Pages: 145-147   Published: MAR-APR 1992
6. Title: ON THE MECHANISM OF PERMANENT BRAIN-DYSFUNCTION IN HYPERPHENYLALANINEMIA
Author(s): HOMMES FA
Source: BIOCHEMICAL MEDICINE AND METABOLIC BIOLOGY   Volume: 46   Issue: 3   Pages: 277-287   Published: DEC 1991
7. Title: VALUE OF NEUROIMAGING IN METABOLIC DISEASES AFFECTING THE CNS
Author(s): NAIDU S, MOSER HW
Source: AMERICAN JOURNAL OF NEURORADIOLOGY   Volume: 12   Issue: 3   Pages: 413-416   Published: MAY-JUN 1991
8. Title: DELAYED CENTRAL-NERVOUS-SYSTEM MYELINATION IN THE SUDDEN-INFANT-DEATH-SYNDROME
Author(s): KINNEY HC, BRODY BA, FINKELSTEIN DM, et al.
Source: JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY   Volume: 50   Issue: 1   Pages: 29-48   Published: JAN 1991
9. Title: ANIMAL-MODEL OF HUMAN-DISEASE - MAPLE SYRUP URINE DISEASE (BRANCHED-CHAIN KETOACIDURIA)
Author(s): HARPER PAW, HEALY PJ, DENNIS JA
Source: AMERICAN JOURNAL OF PATHOLOGY   Volume: 136   Issue: 6   Pages: 1445-1447   Published: JUN 1990
10. Title: NEUROLOGICAL DETERIORATION IN ADULT PHENYLKETONURIA
Author(s): VILLASANA D, BUTLER IJ, WILLIAMS JC, et al.
Source: JOURNAL OF INHERITED METABOLIC DISEASE   Volume: 12   Issue: 4   Pages: 451-457   Published: 1989